A Case report of a young girl with Fibrous dysplasia (FD) concomitant with secondary Aneurysmal bone cyst (ABC)

Authors

  • Hussain Wahab Alanfees Medical college and hospital Author
  • Azar Birlas Northwest General Hospital and Research center, Peshawar Author
  • Muhammad Ibrahim Northwest General Hospital and Research center, Peshawar Author
  • Nuzhat Sultana Khattak Northwest School of medicine, Peshawar Author
  • Raja Irfan Qadir Northwest General Hospital and Research center, Peshawar Author

Abstract

Background:Fibrous dysplasia is a bone disorder in which normal matrix of bone is replaced by fibrous tissue. Most common bones effected are ribs, long bones and pelvis. A benign type of bone lesion known as Aneurysmal bone cyst (ABC). Common bones affected by ABC are tibia and femur. Concomitant Fibrous dysplasia with secondary ABC is long bones is very rare.

Case Report:We are presenting a case report of 22 years old girl, who presented with pain right thigh and leg. Work up was done and based on radiological findings, diagnosed with Fibrous dysplasia (F.D). Surgery was planned for curettage and bone grafting. Per op there was blood filled sinus and fibrous septa, Biopsy was sent, it turned out to be fibrous dysplasia concomitant with secondary ABC.

Discussion:Concomitant FD with Secondary ABC is rare. After through literature review, we could identify two cases of concomitants FD with ABC in long bones.

References

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Published

2023-06-09

How to Cite

A Case report of a young girl with Fibrous dysplasia (FD) concomitant with secondary Aneurysmal bone cyst (ABC). (2023). Journal of Pakistan Orthopaedic Association, 35(2), 23-27. https://jpoa.org.pk/index.php/upload/article/view/713